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. 2017 Nov 30;17(4):557–564. doi: 10.1007/s10689-017-0062-2

Table 1.

Study characteristics

Study Year Germline mutation or Amsterdam only Total cases Gender (male %) Mean follow-up Mean age diagnosis Range of age of diagnosis Segmental Colectomy MCC after Segmental colectomy Extended colectomy MCC after Extended colectomy
Kalady [34] 2012 Amsterdam 296 47.9 104 47.9 253 55 43 3
Van Dalen [35] 2003 Amsterdam 93 n/a 156 47 26–81 70 16 23 0
Cirillo [32] 2013 Amsterdam 65 58.5 72 47 54 15 11 2
Vasen [36] 1993 Amsterdam 54 n/a 69.6 45 17–88 37 8 17 2
Parry [13] 2011 Germline 382 51 108 46 332 74 50 0
Cappel [37] 2002 Germline 139 n/a 81.6 46 24–78 110 13 29 1
Natarajan [38] 2010 Germline 106 39.6 144 45.5 69 23 37 4
Kim [39] 2017 Germline 106 52.8 68.1 43.5 24–82 76 13 30 0
Win [25] 2013 Germline 88 44 132 42.8 79 21 9 0
Stupart [28] 2011 Germline 60 59.2 72 44 39 8 21 0