Table 1. Systemic vasculitis classification according to the Revised International Chapel Hill Consensus Conference Nomenclatures of Vasculitides (9).
Large calibre |
Takayasu’s arteritis |
Giant cell arteritis |
Medium calibre |
Polyarteritis nodosa |
Kawasaki disease |
Small calibre |
ANCA |
Granulomatosis with polyangiitis |
Microscopic polyangiitis |
Eosinophilic granulomatosis with polyangiitis |
Immune complexes |
Anti-basement membrane antibody disease |
Cryoglobulinemic vasculitis |
Henoch-Schönlein purpura |
Hypocomplementemic urticarial vasculitis |
Various calibres |
Behçet disease |
Cogan syndrome |
Vasculitis-associated with other organs |
HBV and HCV associated vasculitis |
Lupus vasculitis |
Rheumatoid vasculitis |
Sarcoidosis vasculitis |
Eosinophilic aortitis |
Drug-induced vasculitis |
Neoplastic vasculitis |
Single-organ vasculitis |
Cutaneous leukocytoclastic vasculitis |
Cutaneous arteritis |
Primary CNS vasculitis |
Aortitis |
ANCA, antineutrophil cytoplasm antibodies; CNS, central nervous system; HBV, hepatitis B virus; HCV, hepatitis C virus.