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. 2018 Sep;10(9):5560–5575. doi: 10.21037/jtd.2018.08.117

Table 1. Systemic vasculitis classification according to the Revised International Chapel Hill Consensus Conference Nomenclatures of Vasculitides (9).

Large calibre
   Takayasu’s arteritis
   Giant cell arteritis
Medium calibre
   Polyarteritis nodosa
   Kawasaki disease
Small calibre
   ANCA
      Granulomatosis with polyangiitis
      Microscopic polyangiitis
      Eosinophilic granulomatosis with polyangiitis
   Immune complexes
      Anti-basement membrane antibody disease
      Cryoglobulinemic vasculitis
      Henoch-Schönlein purpura
      Hypocomplementemic urticarial vasculitis
Various calibres
   Behçet disease
   Cogan syndrome
Vasculitis-associated with other organs
   HBV and HCV associated vasculitis
   Lupus vasculitis
   Rheumatoid vasculitis
   Sarcoidosis vasculitis
   Eosinophilic aortitis
   Drug-induced vasculitis
   Neoplastic vasculitis
Single-organ vasculitis
   Cutaneous leukocytoclastic vasculitis
   Cutaneous arteritis
   Primary CNS vasculitis
   Aortitis

ANCA, antineutrophil cytoplasm antibodies; CNS, central nervous system; HBV, hepatitis B virus; HCV, hepatitis C virus.