Table 2.

The Relapsing Polychondritis Disease Activity Index (RPDAI), adapted from Arnaud et al ⁹

Points		Points
	Constitutional symptoms		Cutaneous manifestations
2	Fever (>38°C/100.4°F)	3	Purpura
	Rheumatological manifestations		Renal manifestations
1	Arthritis	4	Haematuria
	Chondritides	6	Proteinuria
3	Manubriosternal chondritis	17	Renal failure
4	Sternoclavicular chondritis		Cardiovascular manifestations
4	Costochondritis	9	Pericarditis
9	Auricular chondritis (can be unilateral or bilateral)	16	Large-sized and/or medium-sized vessel involvement
9	Nasal chondritis	17	Myocarditis
	Ophthalmological manifestations	18	Acute aortic or mitral insufficiency
5	Episcleritis		Neurological manifestations
9	Scleritis	12	Motor or sensorimotor neuropathy
9	Uveitis	22	Encephalitis
11	Corneal ulcer		Respiratory manifestations
14	Retinal vasculitis		Respiratory chondritis (laryngeal and/or tracheal and/or bronchial chondritis)
	Biological data	14	Without acute respiratory failure
3	Raised C reactive protein (>20 mg/L)	24	With acute respiratory failure
	ENT manifestations		Other (please explain):
8	Sensorineural deafness
12	Vestibular dysfunction
			TOTAL RPDAI SCORE

The scoring should only take into account manifestations attributable to relapsing polychondritis and present during the last 28 days.

ENT, ear, nose and throat.