| Syndrome |
Age of onset |
Seizure type |
EEG findings |
|
Ohtahara Syndrome
(epileptic encephalopathy)
|
First three months
(usually within first 10 days of birth)
|
Tonic/clonic, clonic, myoclonic, atonic, absences, partial, complex partial (with or without secondary generalization) |
Burst and suppression pattern during both waking and sleeping states. |
|
West Syndrome
(epileptic encephalopathy)
|
4–6 months |
Epileptic spasms |
Hypsarrthymia |
| Dravet Syndrome (severe myoclonic epilepsy) |
First year |
Focal or secondarily generalized with fever in infancy; myoclonus after 1 year of age |
Often normal at onset; generalized spikes/polyspikes activated with a photic stimulation |
| Pseudo-Lennox-Gastaut Syndrome (atypical benign partial epilepsy) |
Early childhood
|
Atypical absence, myoclonus, atonic, and focal seizures
|
Rolandic sharp waves, multifocal sharp waves, electrical status epilepticus in sleep |
|
Doose Syndrome (myoclonic-atonic epilepsy)
|
Early childhood
|
Myoclonic-atonic, myoclonus, and atypical absence
|
2–3 Hz generalized spike-waves, photo-paroxysmal response |
| Electrical Status Epilepticus during Slow Sleep (ESES) |
Two months - 12 years (peak age 4 and 5 years) |
Unilateral or bilateral clonic, generalized tonic-clonic, absences, complex partial seizures, with or without drop attacks |
Spikes and waves occurring almost continuously during slow sleep (subclinical) |
| Acquired Epileptic Aphasia Landau-Kleffner Syndrome (LKS) |
18 months – 13 years |
Generalized tonic-clonic seizures |
Paroxysmal electroencephalographic changes and little or no language development |
| Juvenile Myoclonic Epilepsy |
Adolescence |
Myoclonic jerks with or without generalized tonic-clonic seizures and/or absence seizures |
3-5 Hz generalized spike waves and polyspikes with normal background activity |
