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. Author manuscript; available in PMC: 2019 Sep 1.
Published in final edited form as: Am J Med Genet C Semin Med Genet. 2018 Jul 28;178(3):326–337. doi: 10.1002/ajmg.c.31638

Figure 2. : Pleural and lymphatic involvement in LAM.

Figure 2

2A: CT chest in a patient with TSC-LAM showing a spontaneous pneumothorax. 2B: CT chest demonstrating right sided pleural effusion that was confirmed as a chylothorax following thoracentesis. 2C: CT chest showing ground glass attenuation in the right lower lobe suggestive of chylous congestion in a patient with LAM and history of chyloptysis. 2B and 2C: The chylous effusion as well as the chylous congestion resolved successfully after treating with sirolimus.