Table 2.
Laboratory and biochemical data
Age (years) | Laboratory references | ||||||
---|---|---|---|---|---|---|---|
Hb | PLT | AST | ALT | INR | AFP | D-/L-arabitol enantiomer ratio | |
0–2 weeks, 14.9–23.7; 2 weeks–2 months, 13.4–9.8; 2–6 months, 9.4–13; 6 months–1 year, 11.1–14.1; 1–2 years, 11.3–14.1; 2–6 years, 11.5–13.5; 6–12 years, 11.5–15.5; 12–18 years, boys, 13–16 mg/dL | 150–450 × 103/μL | <52 U/L | <18 months, N < 55/60 U/L; 18 months–12 years, boys, N < 40 U/L; >12 years, boys, N < 26 U/L | 0.9–1.2 | <5.0 IU/mL | <3.0 mmol/mol creatinine | |
Patient I | |||||||
1.3 | 11.2–12.0 | 47 | 141–258 | 68–146 | 1.49 | 2,100 | n.a. |
3.5 | 12.5 | 80 | 173–190 | 95–136 | 1.52–1.87 | 620 | 14.5 |
5.5 | 10.2–11.5 | 59 | 82 | 44 | 1.34 | 57.4 | 9.15 |
7.5 | 8.2–10.4 | 59–71 | 66–132 | 27–40 | 1.31–1.45 | n.a. | n.a. |
10.0 | 11.3 | 83 | 76 | 36 | 1.48 | 7.5 | n.a. |
11.0 | 10.4 | 75 | 109 | 62 | 1.48 | 5.4 | 8.2 |
12.5 | 11.1 | 99 | 91 | 66 | 1.51 | 5.1 | n.a. |
Patient II | |||||||
0.1 | 8.6 | 104 | 55–84 | 66–87 | n.a. | 45,450 | n.a. |
0.4 | 11.2 | 116 | 94 | 105 | 1.27 | 21,618 | 13.0 |
1.8 | 8.7 | 78 | 277 | 113 | 2.08 | n.a. | n.a. |
4.5 | 10.7–11.4 | 83 | 227 | 82 | 1.60 | n.a. | n.a. |
6.0 | 10.0 | 155 | 258 | 80 | 1.56 | 64.1 | n.a. |
8.0 | 12.4 | 127 | 115 | 58 | 1.53 | 44.3 | 7.8 |
9.5 | 13.5 | 126 | 139 | 65 | 1.51 | 31.6 | n.a. |
Patient III | |||||||
0.1 | 11.2–15.9 | 31–125 | 90 | 72 | 1.88 | n.a. | 8.50 |
0.7 | 11.3 | 117 | 71 | 39 | 1.85 | n.a. | 8.37 |
1.0 | 11.1 | 126 | 133 | 60 | 1.32 | 49.3 | n.a. |
2.0 | 11.6 | 101 | 58 | 38 | 1.23 | 44.8 | n.a. |
7.0 | 11.6 | 106 | 28 | 16 | 1.10 | 4.62 | 7.5 |
Patient IV | |||||||
0.1 | 11.1 | 35 | 84–97 | 24–30 | 1.92 | n.a. | n.a. |
0.3 | 11.5 | 66 | 72 | 33 | 1.49 | n.a. | n.a. |
1.0 | 12.0 | 64 | 168 | 50 | 1.81 | 278 | n.a. |
1.4 | 12.6 | 59 | 163 | 42 | 1.65 | n.a. | 13.2 |
2.0 | 11.6 | 85 | 192 | 45 | 1.69 | 150 | 11.7 |
4.0 | 11.2 | 63 | 213 | 55 | 1.50 | 102 | n.a. |