Skip to main content
. 2018 Jan 3;42:79–87. doi: 10.1007/8904_2017_83

Table 2.

Laboratory and biochemical data

Age (years) Laboratory references
Hb PLT AST ALT INR AFP D-/L-arabitol enantiomer ratio
0–2 weeks, 14.9–23.7; 2 weeks–2 months, 13.4–9.8; 2–6 months, 9.4–13; 6 months–1 year, 11.1–14.1; 1–2 years, 11.3–14.1; 2–6 years, 11.5–13.5; 6–12 years, 11.5–15.5; 12–18 years, boys, 13–16 mg/dL 150–450 × 103/μL <52 U/L <18 months, N < 55/60 U/L; 18 months–12 years, boys, N < 40 U/L; >12 years, boys, N < 26 U/L 0.9–1.2 <5.0 IU/mL <3.0 mmol/mol creatinine
Patient I
1.3 11.2–12.0 47 141–258 68–146 1.49 2,100 n.a.
3.5 12.5 80 173–190 95–136 1.52–1.87 620 14.5
5.5 10.2–11.5 59 82 44 1.34 57.4 9.15
7.5 8.2–10.4 59–71 66–132 27–40 1.31–1.45 n.a. n.a.
10.0 11.3 83 76 36 1.48 7.5 n.a.
11.0 10.4 75 109 62 1.48 5.4 8.2
12.5 11.1 99 91 66 1.51 5.1 n.a.
Patient II
0.1 8.6 104 55–84 66–87 n.a. 45,450 n.a.
0.4 11.2 116 94 105 1.27 21,618 13.0
1.8 8.7 78 277 113 2.08 n.a. n.a.
4.5 10.7–11.4 83 227 82 1.60 n.a. n.a.
6.0 10.0 155 258 80 1.56 64.1 n.a.
8.0 12.4 127 115 58 1.53 44.3 7.8
9.5 13.5 126 139 65 1.51 31.6 n.a.
Patient III
0.1 11.2–15.9 31–125 90 72 1.88 n.a. 8.50
0.7 11.3 117 71 39 1.85 n.a. 8.37
1.0 11.1 126 133 60 1.32 49.3 n.a.
2.0 11.6 101 58 38 1.23 44.8 n.a.
7.0 11.6 106 28 16 1.10 4.62 7.5
Patient IV
0.1 11.1 35 84–97 24–30 1.92 n.a. n.a.
0.3 11.5 66 72 33 1.49 n.a. n.a.
1.0 12.0 64 168 50 1.81 278 n.a.
1.4 12.6 59 163 42 1.65 n.a. 13.2
2.0 11.6 85 192 45 1.69 150 11.7
4.0 11.2 63 213 55 1.50 102 n.a.