Table 1.
Case | Clinical presentation | Initial diagnosis | Treatment | Serum IgG4 level |
---|---|---|---|---|
1 | Paravertebral mass | Inflammatory myofibroblastic tumor Idiopathic retroperitoneal fibrosis |
Oral cyclophosphamide Mycophenolate mofetil Steroid and rituximab |
0.604 mg/dl (after treatment) Pretreatment level is not available |
2 | Parotid mass Pachymeninges |
Inflammatory pseudotumor Non-Hodgkin's lymphoma |
Steroid and rituximab Proton therapy |
14.2 mg/dl after steroid treatment Pretreatment level is not available |
3 | Proptosis Lacrimal and salivary gland swelling |
Mikulicz syndrome | Steroid and azathioprine | 340 mg/dl Pretreatment level |
4 | Recurrent pancreatitis | Ampullary adenoma | Whipple's procedure Steroid and rituximab |
149 mg/dl Pretreatment level |