Table 3.
Patient characteristics based on ependymal tumor subgroups
SP-SE | SP-MPE | SP-EPN | PF-SE | PF-EPN-A | PF-EPN-B | ST-SE | ST-EPN-RELA | |
---|---|---|---|---|---|---|---|---|
Number n (%) | 5 (4.1) | 29 (23.8) | 32 (26.2) | 24 (19.7) | 1 (0.8) | 13 (10.7) | 14 (11.5) | 4 (3.3) |
Age, y (median range) | 59 (46–73) | 43 (18–80) | 42 (24–69) | 54 (18–79) | 42 (42–42) | 37 (19–63) | 49 (26–73) | 37 (26–62) |
Sex | ||||||||
Male | 2 (40.0) | 20 (69.0) | 17 (53.1) | 23 (95.8) | 1 (100.0) | 6 (46.2) | 11 (78.6) | 2 (50.0) |
Female | 3 (60.0) | 9 (31.0) | 15 (46.9) | 1 (4.2) | 0 | 7 (53.8) | 3 (21.4) | 2 (50.0) |
Karnofsky performance score | ||||||||
<70 | 0 | 0 | 0 | 1 (4.2) | 0 | 0 | 0 | 0 |
70–80 | 2 (66.7) | 11 (52.4) | 10 (41.7) | 8 (33.3) | 1 (100.0) | 3 (25.0) | 6 (46.2) | 0 |
90–100 | 1 (33.3) | 10 (47.6) | 14 (58.3) | 15 (62.5) | 0 | 9 (75.0) | 7 (53.8) | 3 (100.0) |
No data | 2 | 8 | 8 | 1 | 1 | 1 | ||
Surgery | ||||||||
Total | 4 (80.0) | 25 (86.2) | 28 (87.5) | 17 (70.8) | 0 | 9 (69.2) | 12 (85.7) | 3 (75.0) |
Subtotal | 1 (20.0) | 4 (13.8) | 3 (9.4) | 7 (29.2) | 1 (100.0) | 4 (30.8) | 2 (14.3) | 1 (25.0) |
Partial | 0 | 0 | 1 (3.1) | 0 | 0 | 0 | 0 | 0 |
Histology | ||||||||
Subependymoma | 3 (60.0) | 0 | 0 | 7 (29.2) | 0 | 0 | 13 (92.9) | 0 |
Myxopapillary ependymoma | 0 | 14 (48.3) | 0 | 0 | 0 | 0 | 0 | 0 |
Ependymoma | 1 (20.0) | 15 (51.7) | 32 (100.0) | 17 (70.8) | 1 (100.0) | 7 (53.8) | 1 (7.1) | 0 |
Anaplastic ependymoma | 1 (20.0) | 0 | 0 | 0 | 0 | 6 (46.2) | 0 | 4 (100.0) |
RELA fusion-positive | 0 | 0 | 0 | 0 | 0 | 0 | 0 | 4 (100.0) |
WHO 2016 grade | ||||||||
I | 3 (60.0) | 14 (48.3) | 0 | 7 (29.2) | 0 | 0 | 13 (92.9) | 0 |
II | 1 (20.0) | 15 (51.7) | 32 (100.0) | 17 (70.8) | 1 (100.0) | 7 (53.8) | 1 (7.1) | 0 |
III | 1 (20.0) | 0 | 0 | 0 | 0 | 6 (46.2) | 0 | 4 (100.0) |
Localization | ||||||||
Intracranial—supratentorial | 0 | 0 | 0 | 0 | 0 | 0 | 14 (100.0) | 4 (100.0) |
Intracranial—infratentorial | 1 (20.0) | 0 | 0 | 24 (100.0) | 1 (100.0) | 12 (92.3) | 0 | 0 |
Spinal | 4 (80.0) | 29 (100.0) | 32 (100.0) | 0 | 0 | 0 | 0 | 0 |
Disseminated | 0 | 0 | 0 | 0 | 0 | 1 (7.7) | 0 | 0 |
First-line therapy beyond surgery | ||||||||
RT alone (including cyber knife) | 0 | 2 (6.9) | 1 (3.1) | 2 (8.3) | 0 | 8 (61.5) | 0 | 2 (50.0) |
None | 5 (100.0) | 27 (93.1) | 31 (96.9) | 22 (91.7) | 1 (100.0%) | 5 (38.5) | 14 (100.0) | 2 (50.0) |
Progression | ||||||||
Events, n (%) | 0 | 6 (20.7) | 2 (6.3) | 3 (12.5) | 0 | 7 (53.8) | 1 (7.1) | 3 (75.0) |
Death | ||||||||
Events, n (%) | 0 | 2 (6.9) | 1 (3.1) | 2 (8.3) | 0 | 3 (23.1) | 2 (14.3) | 3 (75.0) |