Table 1.

Patient and PN characteristics at baseline and maximum volumetric assessments

Patient Characteristics (n = 41)
Age at enrollment, y
Median (min, max)	13 (5.2, 31.3)
Lower quartile, upper quartile	9.9, 17.0
Number of PN per patient
Median (min, max)	1 (1, 3)
Sex, n (%)
Male	26 (63)
Female	15 (37)
Time between baseline and maximum assessments, y
Median (min, max)	6.5 (0.7, 12.6)
Lower quartile, upper quartile	3.8, 9.1
PN Characteristics (n = 57)
Baseline PN volume, ml
Median (min, max)	238 (2.3, 4895)
Lower quartile, upper quartile	65.4, 674
Baseline PN weight adjusted volume, mL/kg
Median (min, max)	9.9 (0.1, 164.8)
Lower quartile, upper quartile	2.36, 30.0
Maximum PN volume, mL
Median (min, max)	489 (10.2, 7210)
Lower quartile, upper quartile	152, 1329
Max PN weight adjusted volume, mL/kg
Median (min, max)	11.2 (0.3, 198.3)
Lower quartile, upper quartile	2.8, 34
Potential motor PN, n (%)	42 (74)
Orbital PN, n (%)	8 (14)
PN >20% volume change, n (%)	49 (86)