Table 1.

Proposed Shanghai Score System for diagnosis of early repolarization syndrome.

	Points
I. Clinical History
Unexplained cardiac arrest, documented ventricular fibrillation or polymorphic ventricular tachycardia Suspected arrhythmic syncope Syncope of unclear mechanism/unclear etiology	3 2 1
II. Twelve-Lead ECG
Pattern A: ER ≥ 0.2 mV in ≥ 2 inferior and/or lateral ECG leads with horizontal/ descending ST segment. Pattern B: Dynamic changes in J-point elevation (≥0.1 mV) in ≥ 2 inferior and/or lateral ECG leads. Pattern C: ≥ 0.1 mV J-point elevation in at least 2 inferior and/or lateral ECG leads.	2 1.5 1
III. Ambulatory ECG Monitoring
Short-coupled premature ventricular contractions with R on ascending limb or peak of T wave	2
IV. Family History
Relative with definite ERS ≥2 first-degree relatives with a II.A. ECG pattern First-degree relative with a II.A. ECG pattern Unexplained sudden cardiac death ,45 years in a first- or second-degree relative	2 2 1 0.5
V. Genetic Test Result
Probable pathogenic ERS susceptibility mutation	0.5
Score (requires at least 1 ECG finding)
≥ 5 points: Probable/ definite early repolarization syndrome 3–4.5 points: Possible early repolarization syndrome <3 points: Nondiagnostic