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. 2018 Nov 13;16:70. doi: 10.1186/s12969-018-0286-1

Table 3.

Primary or Secondary Diagnoses of Most Common Symptoms in Patients with Secondary and No diagnosis of JDM from 2002 to 2012

Rank ICD-9-CM Codea Diagnosis Weighted
Frequency
Row Prevalence [95% CI]
710.3 as Secondary Diagnosis
 1 782.1 Rash 44 1.87 [0.65–3.10]
 2 728.87 Muscle Weakness 40 1.72 [0.39–3.05]
 3 729.1 Muscle Pain 30 1.30 [0.33–2.28]
 4 780.6 Fever 96 4.14 [2.26–6.01]
 5 787.20 Dysphagia 45 1.94 [0.43–3.46]
 6 784.42 Dysphonia 0
 7 789.00 Abdominal Pain 23 0.97 [0.11–1.83]
 8 CCS 204 Arthritis NOS 80 3.44 [1.86–5.02]
 9 709.3 Calcinosis 27 1.14 [0.06–2.23]
 10 578.1 Melena 8 0.36 [0.00–0.86]
 11 783.0 Anorexia 10 0.43 [0.00–1.04]
No Diagnosis of 710.3
 1 782.1 Rash 166,932 0.73 [0.68–0.77]
 2 728.87 Muscle Weakness 8152 0.04 [0.03–0.04]
 3 729.1 Muscle Pain 31,879 0.14 [0.13–0.15]
 4 780.6 Fever 621,463 2.70 [2.53–2.87]
 5 787.20 Dysphagia 64,240 0.28 [0.23–0.32]
 6 784.42 Dysphonia 1836 0.01 [0.00–0.01]
 7 789.00 Abdominal Pain 159,317 0.69 [0.65–0.73]
 8 CCS 204 Arthritis NOS 136,958 0.59 [0.56–0.63]
 9 709.3 Calcinosis 1025 0.0044 [0.0036–0.0053]
 10 578.1 Melena 59,509 0.26 [0.24–0.28]
 11 783.0 Anorexia 67,501 0.29 [0.25–0.33]

aExcluded repeat diagnosis of JDM

ICD9-CM International Classification of Diseases, Ninth Revision, Clinical Modification; 95% CI 95% confidence interval; NOS Not Otherwise Specified