Table 1. The demographic data, average dystonia age-adjusted prevalence and crude prevalence in different age groups 2007–2016.
Prevalence | Crude prevalence per million ± SD in different age groups | ||||||
---|---|---|---|---|---|---|---|
Dystonia type | per million ± SD (n) | M:F | Age at diagnosis day (n) | 20–39 years | 40–59 years | 60–79 years | over 80 years |
All dystonia | 405 ± 46 (781) | 1:2,7 | 54 ± 12 (1115) | 91 ± 6 | 650 ± 37 | 889 ± 146 | 415 ± 83 |
Focal cervical | 304 ± 34 (589) | 1:2,9 | 53 ± 11 (793) | 64 ± 3 | 527 ± 31 | 641 ± 109 | 220 ± 49 |
Focal upper cranial | 26 ± 5 (47) | 1:2,7 | 64 ± 13 (78) | 2 ± 2 | 14 ± 4 | 74 ± 8 | 138 ± 39 |
Focal upper limb | 15 ± 7 (31) | 1:1,1 | 51 ± 13 (81) | 11 ± 2 | 31 ± 14 | 19 ± 10 | 2 ± 5 |
Focal laryngeal | 12 ± 5 (22) | 1:2,1 | 59 ± 17 (42) | 4 ± 2 | 14 ± 5 | 23 ± 9 | 34 ± 18 |
Focal lower cranial | 5 ± 2 (9) | 1:1,4 | 54 ± 12 (16) | 1 ± 1 | 7 ± 3 | 13 ± 5 | 0 ± 0 |
Focal lower limb | 1 ± 1 (2) | 1:2 | 52 ± 15 (6) | 1 ± 1 | 1 ± 1 | 1 ± 2 | 0 ± 0 |
Focal axial | 1 ± 1 (2) | 1:1 | 62 ± 18 (3) | 0 ± 0 | 2 ± 1 | 2 ± 1 | 8 ± 7 |
Segmental | 33 ± 5 (63) | 1:3,7 | 58 ± 12 (78) | 4 ± 1 | 40 ± 6 | 99 ± 10 | 12 ± 12 |
Multifocal | 6 ± 2 (11) | 1:13 | 52 ± 14 (12) | 3 ± 1 | 8 ± 3 | 14 ± 3 | 0 ± 0 |
Generalized | 2 ± 1 (5) | 1:2,5 | 49 ± 12 (6) | 1 ± 1 | 6 ± 1 | 3 ± 1 | 0 ± 0 |
Average population over 20 years 2007–2016: 1580758. M:F = male: female -ratio. M:F was not counted for dystonia types with less than 10 patients.