Table 1.
Characteristic | All cases (n=245)
|
Adrenal (n=62)
|
Peripheral nerves (n=118)
|
Brain (n=33)
|
Other sites (n=32)
|
|||||
---|---|---|---|---|---|---|---|---|---|---|
No. | % | No. | % | No. | % | No. | % | No. | % | |
|
||||||||||
Age at diagnosis | ||||||||||
< 1 month | 31 | 13% | 15 | 24% | 13 | 11% | 0 | 0 | 3 | 9% |
1 month - 1 year | 75 | 31% | 17 | 27% | 44 | 37% | 6 | 18% | 8 | 25% |
>1 year | 139 | 57% | 30 | 48% | 61 | 57% | 27 | 82% | 21 | 66% |
Mean (months) | 32.9 ± 48.5 | 18.0 ± 21.9 | 23.4 ± 31.0 | 92.4 ± 82 | 36.0 ± 49.5 | |||||
Gender | ||||||||||
Male | 131 | 53% | 37 | 60% | 61 | 52% | 17 | 52% | 16 | 50% |
Female | 114 | 47% | 25 | 40% | 57 | 48% | 16 | 48% | 16 | 50% |
Birth year | ||||||||||
1973-1979 | 85 | 35% | 17 | 27% | 48 | 41% | 14 | 42% | 6 | 19% |
1980-1989 | 92 | 38% | 22 | 35% | 43 | 36% | 15 | 45% | 12 | 38% |
1990-1995 | 68 | 28% | 23 | 37% | 27 | 23% | 4 | 12% | 14 | 44% |
Year of diagnosis | ||||||||||
1973-1979 | 54 | 22% | 14 | 23% | 33 | 28% | 4 | 12% | 3 | 9% |
1980-1989 | 89 | 36% | 21 | 34% | 46 | 39% | 12 | 36% | 10 | 31% |
1990-1995 | 102 | 42% | 27 | 44% | 39 | 33% | 17 | 52% | 19 | 59% |
Survival after diagnosis | ||||||||||
<3 years | 43 | 18% | 18 | 29% | 20 | 17% | 1 | 3% | 4 | 13% |
3+ years | 202 | 82% | 44 | 71% | 98 | 83% | 32 | 97% | 28 | 88% |
Prognosis 1 | ||||||||||
Favorable | 82 | 33% | 23 | 37% | 45 | 38% | 5 | 15% | 9 | 28% |
Intermediate | 144 | 59% | 30 | 48% | 65 | 55% | 28 | 85% | 21 | 66% |
Unfavorable | 19 | 8% | 9 | 15% | 8 | 7% | 0 | 0 | 2 | 6% |
Prognosis variable was created based on age at diagnosis and survival, as described in Methods section.