References | Age at onset of CIDP (years) /gender | Treatment and response of CIDP | Treatment and response of MN |
---|---|---|---|
Witte et al. (7) | 43/M | CS, ineffective; PE, improved | CS, ineffective; PE, ineffective; chlorambucil, ineffective |
Kohli et al. (8) | 18/M | CS, improved | CS, ineffective |
Panjwani et al. (9) | 55/M | CS, improved | CS, ineffective; IVIg, ineffective |
Kanemoto et al. (10) | 9/M | CS, improved | CS, improved |
Mobbs et al. (11) | 81/F | PE+CS+AZT, mild improvement | ND |
Wu et al. (12) | 53/F | IVIg+CS+PE, no improvement other than tremor | IVIg+CS+PE, ineffective |
Wu et al. (12) | 62/M | PE, improved; CS, further improvement | PE+CS, improved |
Emsley et al. (13) | 66/M | Spontaneously improved | ACE inhibitor, improved |
Chen et al. (14) | 60/M | CS, improved; cyclophosphamide, further improved | CS+cyclophosphamide, improved |
Smyth et al. (15) | 25/M | PE+MTX, improved | PE+MTX, improved |
Wong et al. (16) | 36/M | IVIg+CS+PE+cyclosporin or tacrolimus, no improvement | IVIg+CS+PE+cyclosporin or tacrolimus, no improvement |
Wong et al. (16) | 33/F | CS, improved | CS+cyclophosphamide, improved |
Doppler et al. (5) | 48/M | IVIg, initial improvement; CS, transiently improved; PE, improved | Complete recovery (treatment efficacy was not well documented) |
The present case | 78/F | CS, ineffective; IVIg, improved | CS, improved |
ACE, angiotensin converting enzyme; AZT, azathioprine; CS, corticosteroids (oral high dose or methylprednisolone pulse therapy); CIDP, chronic inflammatory demyelinating polyneuropathy; CNTN1, contactin-1; CSF, cerebrospinal fluid; F, female; GBS, Guillain-Barré syndrome; IVIg, intravenous immunoglobulin; M, male; MRC, Medical Research Council; MTX, methotrexate; ND, not documented; PE, plasma exchange.