Table 3.

Main characteristics of patients with primary SS presenting with cutaneous vasculitis

Feature	Patients, n (%)
Prevalence (n = 6301)	610 (10)
Female:male ratio (n = 71)	23:1
Age at diagnosis, years (n = 71)	53
Clinical presentation (n = 170)
Cutaneous purpura	149 (88)
Cutaneous ulcers	16 (9)
Urticarial vasculitis	12 (7)
Cutaneous biopsy (n = 174)	80 (46)
Histopathological features (n = 59)
Leucocytoclastic vasculitis	54 (90)
Lymphocytic vasculitis	1 (2)
Capillaritis	1 (2)
Microthrombosis	1 (2)
Necrotizing vasculitis	2 (4)
Immunological profile
Anti-Ro (n = 87)	54 (62)
Anti-La (n = 86)	29 (34)
Cryoglobulins (n = 72)	26 (36)

Variables were not detailed in all studies and the prevalence of a specific feature is stated as the number of cases with that feature/number of cases in which the feature was detailed.