Fig. 1.

Photograph of an Apert syndrome patient, a 9-year-old male. Facial profile: frontal view (A1): hypertelorism, turribrachycephalic cranial profile, horizontal groove above supra orbital ridge (arrows), and a short nose with bulbous tip. Lateral view (A2): retarded maxilla and frontal proptosis (arrows). Intraoral view: anterior view (B1): anterior open bite and poor oral hygiene. Lateral view (B2): retruded maxillary incisors. Upper occlusal view (C1): narrow and triangular shape maxillary arch with Byzantine arch-shaped palate. Lower occlusal view (C2): almost normal U-shaped mandibular arch with thick lingual frenum (arrows). D Plaster dental model: fissure-like palatal groove (arrows). E Hand, incompletely separated and with short fingers even after syndactyly operation performed 3 years ago