Box 1.

Uncommon manifestations in Behçet’s disease

Cardiac – coronary vasculitis, pericarditis, myocarditis, endocarditis, coronary aneurysms, valvular disease and arrhythmias

Pulmonary – pulmonary opacities, haemorrhage, vasculitis, pleural effusions, pulmonary aneurysms, pulmonary hypertension and fibrosing mediastinitis

Renal – mild renal impairment, glomerulonephritis, interstitial nephritis, renal artery aneurysm and amyloidosis

Other associations – MAGIC (mouth and genital ulcers with inflamed cartilage) represents features of relapsing chondritis and mucosal ulcers

Sweet’s syndrome – fever, nodular rashes, and mouth and genital ulcers