Table 1.
Demographic and clinical parameters
| Parameter | |
|---|---|
| Age (years) | 64 (58–71) |
| Gender | 46 (59%) female |
| Ethnicity | 76 (97%) white European |
| Age of onset of symptoms (years) | 54 (48–60) |
| Age at diagnosis of hypogammaglobulinaemia (years) | 58 (51–62) |
| Age of diagnosis of thymoma (years) | 58 (51–62) |
| Clinical features | |
| Bronchiectasis (on chest CT scan) | 35 (45%) |
| Chronic sinusitis | 7 (9%) |
| Autoimmunity | 20 (26%) |
| Red cell aplasia | 8 (10%) |
| Thyroid | 6 (8%) |
| Arthritis | 4 (5%) |
| Myasthenia | 3 (4%) |
| SLE | 3 (4%) |
| Sjögren’s disease | 2 (3%) |
| Died | 7 (9%) |
Figures represent number (percentage) for discrete variables and median (interquartile range) for continuous variables. SLE = systemic lupus erythematosus; CT = computerized tomography.