Table 1.
Patient demographics in SSc cohort.
Characteristic | ||
---|---|---|
Age (years) | 56.45 ± 13.60 | |
Sex | Female | 29 (93.55) |
SSc duration (years) | 7 (1–28) | |
SSc subset | lcSScdcSSc | 3 (9.67)28 (90.33) |
OHIP 49 | 43.68 (21.07) | |
SHAQ | 0.92 (0.73) | |
Autoantibody pattern | ANA positivity (negative for ACA and anti-Scl70) | 2 (6.45) |
ACA | 10 (32.26) | |
Anti-Scl 70 | 18 (58.06) | |
Educational level | Primary school | 20 (64.52) |
High school or more | 11 (35.48) | |
mRSS | Mild/moderate | 22 (70.97) |
Severe/end-stage | 9 (29.03) | |
GI tract involvement | Present | 21 (67.74) |
Joint/tendon involvement | Present | 27 (87.10) |
Muscular involvement | Present | 21 (67.74) |
Digital ulcers | Present | 6 (19.35) |
Peripheral vascular involvement | Present | 27 (87.10) |
Lung involvement | Present | 27 (87.10) |
Chest radiography | Normal | 22 (70.97) |
Intestinal lung disease | 9 (29.03) | |
FVC | 91.23 ± 21.77 | |
DLCO | 68.33 ± 20.16 | |
Estimated sPAP | High | 4 (12.90) |
Heart involvement | Present | 24 (77.42) |
Data are expressed as mean ± standard deviation, absolute number (%), or median (range).
SSc, systemic sclerosis; lcSSc, limited cutaneous systemic sclerosis; dcSSc, diffuse cutaneous systemic sclerosis; OHIP 49, Oral Health Impact Profile 49; SHAQ, Scleroderma Health Assessment Questionnaire; ANA, antinuclear antibodies; ACA, anti-centromere antibodies; Anti-Scl70, anti-Scl70 antibodies; mRSS, modified Rodnan skin score; GI, gastrointestinal; FVC, forced vital capacity, % predicted; DLCO, diffusing capacity for carbon monoxide, % predicted; sPAP, pulmonary artery systolic pressure.