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Table 1.

Features of laterality disturbances.

Right atrial isomerism Left atrial isomerism
Bilateral right bronchi Bilateral left bronchi
Midline liver Midline liver
Asplenia Polysplenia (often functionally asplenic)
Malrotation Malrotation
Two sinoatrial nodes Absent sinoatrial node (complete heart block can occur, but more usually an ectopic atrial rhythm)
By definition total anomalous pulmonary venous connection Interrupted IVC with azygous continuation