Table 1.
Electrophysiological studies of MADD in the two patients
| Motor nerve | Case 1 | Case 2 | |||||
|---|---|---|---|---|---|---|---|
| MNCV(m/s) | dL (ms) | CMAP (mV) | MNCV(m/s) | dL (ms) | CMAP (mV) | ||
| L Median | E-W | 74(≥50.0) | – | 7.2(≥5.0) | 54 | – | 13.0 |
| W-APB | – | 3.3(≤4.2) | 8.5(≥5.0) | – | 3.3 | 13.8 | |
| R Median | E-W | 67 | – | 5.3 | 56 | – | 16.1 |
| W-APB | – | 3.4 | 5.8 | – | 3.0 | 16.9 | |
| L Ulnar | E-W | 66(≥53.0) | – | 7.6(≥5.5) | 53 | – | 11.0 |
| W-ADM | – | 2.1(≤4.2) | 9.5(≥5.5) | – | 2.5 | 12.4 | |
| R Ulnar | E-W | 68 | – | 8.1 | 61 | – | 10.7 |
| W-ADM | – | 2.0 | 8.5 | – | 2.2 | 11.0 | |
| L Peroneal | FH-A | 47(≥38.0) | – | 3.7(≥3.0) | 43 | – | 2.6 |
| A-EBD | – | 3.0(≤6.1) | 5.1(≥3.0) | – | 3.8 | 3.3 | |
| R Peroneal | FH-A | 58 | – | 10.3 | 50 | – | 3.3 |
| A-EBD | – | 3.7 | 12.5 | – | 4.6 | 3.7 | |
| L Tibial | PF-A | 51(≥35.0) | – | 12.0(≥3.0) | 50 | – | 13.6 |
| A-AA | – | 4.8(≤6.1) | 13.9(≥3.0) | – | 4.8 | 165 | |
| R Tibial | PF-A | 56 | – | 11.4 | 52 | – | 11.5 |
| A-AA | – | 4.4 | 11.2 | – | 5.3 | 12.8 | |
| Sensory nerve | SNCV (m/s) | SNAP (uV) | SNCV (m/s) | SNAP (uV) | |||
| L-Median | IIF-W | 59(≥50.8) | 14.4(≥8.0) | 35 | 1.5 | ||
| R-Median | IIF-W | 57 | 11.9 | 48 | 1.1 | ||
| L-Sural | A-SURA | 42(≥41.9) | 15.5(≥7.0) | NR | NR | ||
| R-Sural | A-SURA | 45 | 26.3 | NR | NR | ||
| F wave | F-Lat(ms) | F-Lat(ms) | |||||
| L-Median | 29.5(≤32.0) | 27.31 | |||||
| R- Median | 27.62 | 27.0 | |||||
| H Reflex | H-Lat(ms) | H-Lat(ms) | |||||
| L Tibial | 28.0(< 40.0) | 32.89 | |||||
| R Tibial | 28.0 | 31.26 | |||||
MNCV motor nerve conduction velocity, CMAP compound motor action potential, dL distal motor latency, SNCV sensory nerve conduction velocity, SNAP sensory nerve action potential, L left, R right, E elbow, W wrist, APB abductor pollicis brevis, ADM abductor digiti minimi, FH fibula head, A ankle, EDB extensor digitorum brevis, PF popliteal fossa, AA abductor allucis, IIF second finger, SURA sural, Lat latency, NR no recorded. Normal values are given in brackets