Fig. 2.

Fundus images and visual fields at 52 years old. (A) Fundus photographs show retinal degeneration with bone spicule pigmentation from the posterior pole to the peripheral retina, attenuation of the retinal vessels, and waxy pallor of the optic disc. In addition, drusen-like accumulation in the right and early atrophy in the left maculae are seen. (B) Fluorescein angiograms in the late phase show generalized hyperfluorescence due to transmission defects with hypofluorescent areas observed by the pigment clumps, especially along the vascular arcades. (C) Goldmann visual field testing shows severely constricted visual fields around 10° in the V-4e isopters.