Table II.
American thoracic Society/European respiratory society classification of IIP from 2013.
IIP classification | Pathology |
---|---|
Major IIP | Idiopathic pulmonary fibrosis |
Idiopathic nonspecific interstitial pneumonia | |
Respiratory bronchiolitis interstitial lung disease | |
Desquamative interstitial pneumonia | |
Cryptogenic organized pneumonia | |
Acute interstitial pneumonia | |
Rare IIP | Idiopathic lymphocytic interstitial pneumonia |
Idiopathic pleuroparenchymal fibroelastosis | |
Unclassified IIP | – |
IIP, idiopathic interstitial pneumonia.