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. 2018 Nov 29;17(1):587–595. doi: 10.3892/etm.2018.7030

Table II.

American thoracic Society/European respiratory society classification of IIP from 2013.

IIP classification Pathology
Major IIP Idiopathic pulmonary fibrosis
Idiopathic nonspecific interstitial pneumonia
Respiratory bronchiolitis interstitial lung disease
Desquamative interstitial pneumonia
Cryptogenic organized pneumonia
Acute interstitial pneumonia
Rare IIP Idiopathic lymphocytic interstitial pneumonia
Idiopathic pleuroparenchymal fibroelastosis
Unclassified IIP

IIP, idiopathic interstitial pneumonia.