Table 1.
Cases | Case 1 | Case 2 | Case 3 | Case 4 | Case 5 | Case 6 | Case 7 | Case 8 | Case 9 | Case 10 |
---|---|---|---|---|---|---|---|---|---|---|
Age (years) | 3 | 5 | 6.5 | 3 | 15 | 4 | 4.5 | 3.5 | 3 | 8 |
Age of onset of constipation | 2.5 years | 1 years | 1 month | 6 months | 8 years | 9 months | 1 months | 5 months | 1.5 year | 1 months |
Duration of constipation | 6 months | 4 years | 6.5 years | 2.5 years | 7 years | 3 years | 4.5 years | 3 years | 1.5 years | 8 years |
Other symptoms | Abdominal distention, FTT | Anemia | Abdominal distention, FTT | None | None | FTT, abdominal distention | Abdominal distention | Abdominal distention | Abdominal distention | FTT, abdominal distention |
Barium enema | Dilated colon | Dilated colon | Reversal of rectosigmoid ratio with transition zone | Normal | Reversal of rectosigmoid ratio with transition zone | Dilated colon | Reversal of rectosigmoid ration with transition zone | Normal | Dilated colon | Reversal of rectosigmoid ration with transition zone |
Anorectal manometry | Absent RAIR | Incomplete RAIR | Absent RAIR | Absent RAIR | Absent RAIR | Absent RAIR | Absent RAIR | RAIR present | — | Absent RAIR |
FTT, failure to thrive; RAIR, rectoanal inhibitory reflex.