Table III.
Clinical manifestations presenting organ involvement in specific types of AAV.
| AAV type organ involvement |
GPA n = 41 |
MPA n = 23 |
PR3-ANCA (+) n = 34 |
MPO-ANCA (+) n = 21 |
ANCA (-) n = 7 |
MPO-ANCA (+) and PR3-ANCA (+) n = 2 |
Total n = 64 |
|---|---|---|---|---|---|---|---|
| ENT | 35 (85.37%) | 13 (56.52%) |
29 (85.29%) |
12 (57.14%) |
5 (71.43%) |
2 (100%) |
48 (75%) |
| Eyes | 5 (12.2%) |
3 (13.04%) |
5 (21.74%) |
3 (14.29%) |
0 (0%) |
0 (0%) |
8 (12.5%) |
| Lungs | 32 (78.05%) | 16 (69.57%) |
29 (85.29%) |
15 (71.43%) |
3 (42.86%) |
1 (50%) |
49 (76.56%) |
| Trachea | 4 (9.76%) |
1 (4.35%) |
4 (11.76%) |
1 (4.76%) |
0 (0%) |
0 (0%) |
5 (7.81%) |
| Kidneys | 26 (63.41%) | 21 (91.3%) |
25 (73.53%) |
19 (90.48%) |
3 (42.86%) |
0 (0%) |
47 (73.44%) |
| Cardiovascular system | 8 (19.51%) |
10 (43.48%) |
8 (23.53%) |
10 (47.62%) |
0 (0%) |
0 (0%) |
18 (28.13%) |
| Skin | 12 (29.27%) |
8 (34.78%) |
11 (32.35%) |
8 (38.1%) |
1 (14.26%) |
0 (0%) |
20 (31.25%) |
| Gastrointestinal system |
2 (4.88%) |
3 (13.04%) |
2 (5.88%) |
2 (9.52%) |
1 (14.26%) |
0 (0%) |
5 (7.81%) |
| Musculoskeletal system |
10 (24.39%) | 6 (26.09%) |
10 (29.41%) |
6 (28.57%) |
0 (0%) |
0 (0%) |
16 (25%) |
| Nervous system | 8 (19.51%) |
0 (0%) |
8 (23.53%) |
0 (0%) |
0 (0%) |
0 (0%) |
8 (12.5%) |