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. 2018 Dec;38(6):544–553. doi: 10.14639/0392-100X-2166

Table III.

Susac syndrome classification.

Category Definition
Suspected One triad manifestation
One risk factor*
  1. Female

    1. 20-40 Years

    2. Within 1 year of pregnancy

  2. Characteristic MRI findings

    1. Corpus callosum lesions

    2. Periventricular lesions

Incomplete Two triad manifestations
Complete Three triad manifestations

*: With no known risk factors for arteriosclerosis and/or coagulopathy.

: Clinical triad of encephalopathy, sensorineural hearing loss, and branch retinal artery occlusion. Susac syndrome classification system (from Vishnevskia-dai et al., 2016 31, mod.).