Figure 1.
Metabolic Acidosis Workup Algorithm. PC, pyruvate carboxylase; UOA, urine organic acids; SC, serum carnitine; MSUD, maple syrup urinary disease; FOAD, fatty acid oxidation disorder; PAC, plasma acylcarnitines; FAA, free fatty acids; PAA, plasma amino acids; GDS 1, glycogen storage disorder type 1.
