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. 2018 Dec;6(24):470. doi: 10.21037/atm.2018.11.05

Figure 1.

Figure 1

Metabolic Acidosis Workup Algorithm. PC, pyruvate carboxylase; UOA, urine organic acids; SC, serum carnitine; MSUD, maple syrup urinary disease; FOAD, fatty acid oxidation disorder; PAC, plasma acylcarnitines; FAA, free fatty acids; PAA, plasma amino acids; GDS 1, glycogen storage disorder type 1.