Table 1.

Data on pubertal attainment, maximum height centile, lumbar spine Z score, and BMI according to EB sub‐type and age

	RDEB Sub‐type	Sex	16‐20 y			21‐25 y		26‐30 y		31‐35 y		Puberty (age in years)
			DXA	BMI	MHC	DXA	BMI	DXA	BMI	DXA	BMI
1	SG	M	−4.2	10	25	—		−2.6	14	−2.4	14	Y (NK)
2	SG	F	−1.2	20	0.4‐2	−1.3	19	−1.9	19	—		Y (15)
3	SG	M	—	19	0.4‐2	−3.9	21	−3.0	24	—		Y(15)
4	SG	M	−3.9	14	<0.4	−6.1	14	—		—		N
5	SG	M	−2.9	16	50‐75	−1.5	16	—		—		Y (19)
6	SG	M	—	16	25‐50	−1.75	20	−1.7	23	—	23.5	Y (13)
7	SG	F	−5.3	15	<0.4	−4.5	15	—		—		N
8	SG	F	−3.56	18	0.4	−4.0	—	—	17.5	−2.9	18	Y (16)
9	SG	F	−3.3	16.5	25‐50	−3.5	16.5	—	1	—		Y (15)
10	SG	F	—	22.5	25	−3.3	20	−3.5	19.5	—		Y (13)
11	SG	M	—		0.4	−0.47	21	−1.39	19	—		Y (13)
12	SG	M	−4.7	16	<0.4	−5.6	12	—		—		N
13	SG	F	−2.8	19.5	2	−2.2		−2.2	18	—		Y (13)
14	SG	F	−0.45	15.5	50	−0.9	16	—		—		Y (13)
15	SG	F	−2.3	29	2	−2.3	17.5	−1.2	18	—	18	Y (15)
16	SG	F	—		2	—		−2.6	17.5	−2.7	17	Y (NK)
17	SG	F	—	17	9	−2.6	19.5	—	19.5	—	20	Y (13)
18	SG	F	—	13	50	−3.9	12	—	14			Y (17)
19	SG	M			<0.4					−2.5	19.6	N
20	SG	M			9					−1.86	18.5	Y (19)
21	SG	F			9‐25	—	15	−2.2	—			Y (NK)
22	SG	M	−3.8	22	<0.4							N
23	SG	F			<0.4			−2.0	26.5			Y (16)
24	GI	M	−2.2	15	91	−2.0	16	−1.3	15.5	—		Y (18)
25	GI	M	−0.66	—	50‐75	−0.7	18.5	−0.5	19	—	18.5	Y (14)
26	GI	M	−0.65	24	50	−0.9	24.5	—	24	—		Y (13)
27	GI	M	−0.65	20.5	2‐9	−2.0	22	−2.4	21			Y (NK)
28	GI	F	−3.3	17.5	99							Y (18)
29	GI	F			25					−0.27	20	Y (12)
30	GI	M			91‐98					−0.5	29.5	Y (15)
31	I	M	—		50	−1.2		−1.05	20	−0.7	22.5	Y (13)
32	I	M	—		25‐50	−1.9		−1.9	16.5	−1.4	25.5	Y (13)
33	I	F	−0.7	19.5	50							Y (17)
34	I	F			25			—	31	0.2	25	Y (NK)

DXA, numbers in bold indicate osteoporosis; MHC, maximum height centile attained; NK, not known.