Table 1.

Subject demographics

	Controls	Sporadic bvFTD/MND	C9orf72-bvFTD/MND
N	10	17	10
Clinical diagnoses	N/A	3 ALS, 1 MND, 2 bvFTD-ALS, 5 bvFTD-MND, 6 bvFTD	2 ALS, 5 bvFTD-MND, 3 bvFTD
Neuropathological diagnoses	N/A	4 ALS-TDP; 2 FTLD-TDP-B, ALS; 8 FTLD-TDP-B, MND; 3 FTLD-TDP-B	1 ALS-TDP; 5 FTLD-TDP-B, MND; 3 FTLD-TDP-U, MND; 1 FTLD-TDP-U
Gender (M:F)	6:4	10:7	8:2
Age at death (years)	63.6 (9.8)	61.8 (7.4)	59.8 (3.4)
Symptom duration (years)	N/A	5.2 (2.8)	7.1 (6.9)
PMI (hours)	43.1 (38.2)	13.0 (10.2)	13.3 (6.3)
Broe stage; median (range)	N/A	1 (0-2)	1 (0-2)
Brain weight (g)	1244 (151)	1284 (138)	1257 (172)
CDR total	N/A	1.8 (1.1)	1.3 (0.9)
CDR Sum of boxes	N/A	8.9 (5.2)	7.5 (5.0)
Worst NPI, sum of apathy, disinhibition, motor, eating	N/A	41.9 (25.1)	44.3 (27.5)
IRI, empathic concern subscale	N/A	20.0 (8.0)	17.6 (7.3)

Unless otherwise noted, numbers in parentheses are SD of preceding mean.