Skip to main content
. Author manuscript; available in PMC: 2019 Nov 7.
Published in final edited form as: Semin Respir Crit Care Med. 2018 Nov 7;39(4):413–424. doi: 10.1055/s-0038-1673386

Table 1.

Etiology of pulmonary vasculitis

Most frequent cause
 ANCA vasculitis and granulomatosis
  Granulomatosis with polyangiitis
  Microscopic polyangiitis
  Eosinophilic granulomatosis with polyangiitis
Less frequent causes
 Other systemic vasculitis
  Antiglomerular basement membrane disease
  IgA vasculitis
  Behcet’s disease
  Cryoglobulinemic vasculitis
  Takayasu arteritis
 Autoimmune diseases
  Systemic lupus erythematosus
  Antiphospholipid syndrome
  Sarcoidosis
  Rheumatoid arthritis
 Infections
  Bacteria, e.g., mycobacteria, syphilis, rickettsias
  Fungus, e.g., aspergillosis, histoplasmosis
  Virus, e.g., herpes zoster
  Malignancy
 Drugs-induced ANCA vasculitis
  Propylthiouracil, diphenylhydantoin, levamisole-adulterated cocaine

Abbreviations: ANCA, antineutrophil cytoplasmic antibody; IgA, immunoglobulin A.

Source: Modified from Franks and Koss132 and Heeringa.133