Table 1.

Epilepsy syndromes and some conditions in which the KD therapies has been reported probable benefit^∗.

Angelman syndrome

Complex 1 mitochondrial disorders

Dravet syndrome

Epilepsy with myoclonic–atonic seizures (Doose syndrome)

Glucose transporter protein 1 (Glut-1) deficiency syndrome (Glut1DS)

Febrile infection–related epilepsy syndrome (FIRES)

Formula-fed (solely) children or infants

Infantile spasms

Ohtahara syndrome

Pyruvate dehydrogenase deficiency (PDHD)

Super-refractory status epilepticus

Tuberous sclerosis complex

^∗Adapted from Kossoff et al. (2018). Optimal clinical management of children receiving dietary therapies for epilepsy: Updated recommendations of the International Ketogenic Diet Study Group (Kossoff et al., 2018).