Skip to main content
. Author manuscript; available in PMC: 2019 Feb 21.
Published in final edited form as: Muscle Nerve. 2017 Apr 25;57(1):54–60. doi: 10.1002/mus.25629

Table 1.

Participant demographics

COL6-RD
LAMA2-RD
HV
Characteristics 50-kHZ and
50:200-kHZ
analyses
Phase slope
100–500-kHZ
analyses
50-kHZ and
50:200-kHZ
analyses
Phase slope
100–500-kHZ
analyses
50-kHZ
analysis

No. of participants 21 13 20 16 21
Mean age (years) 12.5 63.8 12.8 63.9 9.4 62.6 9.0 62.7 11.4 62.5
 ±SD (range) (7–20) (7–15) (5–15) (5–15) (7–17)
Male 12 7 9 8 8
Female 9 6 11 8 13
Ambulatory 11 6 4 1 21

COL6-RD, collagen 6-related disorder; HV, healthy volunteer; LAMA2-RD, laminin α-2-related disorder.