Table 1.

Demographics summary of the CPVT- and exercise-associated autopsy negative SUDY cohorts.

	Overall	PKP2 Negative	PKP2 Positive
Patients Diagnosed with CPVT (N)	18	13	5
Males/Females	9/9	7/6	2/3
Average Age (years)	19.6 ± 12.8	19.7 ± 14.7	19.4 ± 6.3
Age Range (years)	6 to 58	6 to 58	12 to 28
Average QTc (ms)	417 ± 26	416 ± 23.4	419 ± 35
Ventricular Ectopy	13 (72%)	8 (61.5%)	5 (100%)
Symptomatic	15 (83%)	10 (77%)	5 (100%)
Syncope	13 (72%)	10 (77%)	3 (60%)
Cardiac Arrest	2 (11%)	0 (0%)	2 (40%)
Exertional Trigger	13 (72%)	8 (61.5%)	5 (100%)
Positive Family History of Cardiac Events (syncope, seizures, cardiac arrest, etc.)	5 (28%)	4 (31%)	1 (20%)
Family History of SCD in the Young (< 40 years of age)	2 (11%)	1 (8%)	1 (20%)
Cases of Exercise-Associated SUDY (N)	19	18	1
Males/Females	13/6	12/6	1/0
Average Age (years)	13.9 ± 3.2	13.8 ± 3.2	16
Age Range (years)	6 to 19	6 to 19	16
Exertion Related Death	19 (100%)	18 (100%)	1 (100%)
Previous Personal History of Cardiac Event	4 (21%)	4 (22%)	0 (0%)
Positive Family History of Cardiac Events (syncope, seizures, cardiac arrest, etc.)	4 (21%)	4 (22%)	0 (0%)
Family History of SCD in the Young (< 40 years of age)	1 (5%)	1 (5.5%)	0 (0%)

SUDY= sudden death in the young; CPVT = catecholaminergic polymorphic ventricular tachycardia; SCD=sudden cardiac death