Table 1.
Baseline Characteristics of Patients With SQTS at Admission
Variables | N=17 |
---|---|
Demographics | |
Age, median (IQR) | 42.45 (0–67) |
Men, No. (%) | 8 (48) |
Symptoms, No. (%) | |
Syncope | 5 (29) |
Palpitation | 8 (47) |
SCD | 3 (17.6) |
Atrial flutter | 2 (12) |
Atrial fibrillation | 7 (41) |
ECG data, mean±SD | |
QTc interval, ms | 324.9±40.8 |
Quinidine, No. (%) | |
Yes | 6 (35) |
ECG after quinidine, mean±SD | |
QTc interval, ms | 409±41.63 |
ICD implantation, No. (%) | |
Yes | 5 (29) |
No | 11 (65) |
Event recorder | 1 (6) |
Genetic screening, No. (%) | |
Unknown mutation | 4 (24) |
Known mutation | 13 (76) |
CaCN2b | 6 (35) |
CaCNA1C | 3 (17) |
KCNH2 | 4 (23) |
SCN5a | 1 (6) |
Positive ajmalin test, No. (%) | 7 (41) |
ICD indicates implantable cardioverter‐defibrillator; IQR, interquartile range; QTc, corrected QT; SCD, sudden cardiac death; SQTS, short QT syndrome.