Table III.

Characteristic of first and diagnostically crucial symptoms along with age at the emergence of first and crucial manifestations and delay of diagnosis in the studied cases

Case	I	II	III	IV	V	VI	VII	VIII	IX	X
Gender	Female	Female	Male	Female	Female	Female	Female	Male	Male	Male
The first symptom	Bronchial stenosis	Nasal chondritis	General symptoms	Laryngeal stenosis	Red ear	Red ear	Laryngeal stenosis	Red ear	Red ear	Arthritis
The diagnostically crucial symptom	Red ear	Red ear	Red ear	Laryngeal stenosis	Red ear	Red ear	Laryngeal stenosis	Red ear	Red ear	Red ear
Age at the emergence of the first symptom	53 years	52 years	58 years	69 years	55 years	55 years	31 years	37 years	45 years	68 years
Age at the diagnosis	58 years	53 years	59 years	73 years	57 years	58 years	32 years	37 years	45 years (RP highly probable)	73 years
Time from the first symptom to the diagnosis	58 months	9 months	6 months	41 months	8 months	21 months	15 months	4 months	2 months	48 months
Time from the crucial symptom to the diagnosis	34 months	2 months	2 months	41 months	8 months	21 months	15 months	4 months	Diagnosis not yet confirmed	15 months