Gender |
Female |
Female |
Male |
Female |
Female |
Female |
Female |
Male |
Male |
Male |
10 |
Auricular chondritis |
Yes (bilateral) |
Yes (bilateral) |
Yes (bilateral) |
No |
Yes (bilateral) |
Yes (bilateral) |
Yes (bilateral) |
Yes (bilateral) |
Yes (bilateral) |
Yes (unilateral) |
9 |
Nasal chondritis |
Yes |
Yes |
Yes |
Yes |
Yes |
Yes |
Yes (nasal bridge collapse) |
No |
No |
No |
7 |
Respiratory tract chondritis |
Yes (bronchial and subglottic stenosis) |
No |
No |
Yes (laryngeal stenosis, tracheotomy, tracheomalacia) |
Yes (laryngeal oedema) |
No |
Yes (laryngeal stenosis, tracheotomy, tracheal and bronchial stenosis) |
No |
No |
Yes (thickening of the bronchial walls) |
5 |
Arthritis |
No |
No |
Yes (confirmed by USG) |
No |
Yes (confirmed by USG) |
No |
Yes (confirmed by USG) |
No |
No |
Yes (confirmed by USG) |
4 |
Ocular inflammation |
No |
No |
Yes (episcleritis) |
No |
Yes (scleritis) |
No |
Yes (scleritis) |
No |
No |
No |
3 |
Audio-vestibular damage |
No |
No |
No |
No |
No |
No |
Yes (hearing loss in the left ear – vestibular damage) |
No |
No |
Yes (progressive hearing loss) |
2 |
Haematological features |
No |
No |
Yes (anaemia) |
Yes (anaemia) |
No |
No |
No |
No |
No |
No |
2 |
Cardiac involvement |
Yes (valvular disease) |
Yes (valvular disease) |
Yes (arrhythmia) |
No |
No |
No |
No |
No |
No |
Yes (valvular disease) |
4 |
Vascular involvement |
No |
No |
Yes (iliac arteries aneurysms) |
Yes (dilatation of the ascending aorta) |
No |
No |
No |
No |
No |
No |
2 |
Renal involvement |
No |
No |
Yes (erythrocyturia) |
No |
No |
No |
No |
No |
No |
No |
1 |
Costal chondritis |
No |
No |
No |
No |
No |
No |
Yes |
No |
No |
No |
1 |
Skin lesions |
No |
No |
No |
No |
No |
No |
No |
No |
No |
No |
0 |
Nervous system involvement |
No |
No |
No |
No |
No |
No |
No |
No |
No |
No |
0 |
General symptoms |
No |
No |
Yes (fever, weight loss, fatigue) |
No |
No |
No |
No |
No |
No |
No |
1 |
Total number of manifestations |
4 |
3 |
9 |
3 |
3 |
2 |
8 |
1 |
1 |
5 |
– |