Table 5.

Dose-dependent treatment effects in acquired angioedema C1-inhibitor patients without (N = 6) and with (N = 8) anti-C1-INH autoantibodies

	Patients without autoantibodies against C1-INH (N = 6)						Patients with autoantibodies against C1-INH (N = 8)
pdC1-INH dose (U)	No. of patients	No. of attacks	Effectively treated patients	Effectively treated attacks	Non-effectively treated patients	Non-effectively treated attacks	No. of patients	No. of attacks	Effectively treated patients	Effectively treated attacks	Non-effectively treated patients	Non-effectively treated attacks
500	3	338	3	337	1	1	7	102	5	33	3	69
1000	4	8	3	7	1	1	6	907	5	900	3	7
1500	0	0	0	0	0	0	2	4	1	1	1	3
2000	0	0	0	0	0	0	4	315	3	311	1	4
3000	0	0	0	0	0	0	1	1	1	1	0	0
	-.	346	–	344	2	2	–	1329	–	1246	–	83

Note: The same patients may be represented as effectively treated and non-effectively treated

C1-INH = C1-inhibitor