a) ADAMTS13 and b) von Willebrand factor (VWF) antigen (Ag) levels by diagnostic group. Dunn's test with false discovery rate adjustment was used to calculate p-values. Healthy control, n=68; chronic thromboembolic pulmonary hypertension (CTEPH), n=208; chronic thromboembolic disease (CTED), n=35; idiopathic pulmonary arterial hypertension (IPAH), n=28; pulmonary embolism (PE), n=28. *: p≤0.05; **: p≤0.01; ***: p≤0.001; ****: p≤0.0001; ns: nonsignificant.