Table 1.
Epidemiology of selected SAIDs as reported by the participating departments.
| SAID | median number of patients seen within the last 12 months |
median age of onset (years) | mean percentages for females | |||
|---|---|---|---|---|---|---|
| by all disciplines | by pediatricians | by dermatologists | by rheumatologists | |||
| CAPS | 2 (1–3.75) | 2 (1–3.5) | 1 (0.5–3) | 3 (1–4) | 20 (10–30) | 64.7 ± 28.8 |
| FMF | 10 (3–20) | 20 (10–52) | 2 (0.5–5) | 6 (3–13) | 14.5 (10–29.75) | 56.3 ± 28.9 |
| HIDS/MKD | 0 (0–1) | 1 (0–2) | 0 (0–0.75) | 0 (0–1) | 8 (2–24) | 61.1 ± 48.6 |
| TRAPS | 1 (1–2) | 1.5 (0.75–2.25) | 1 (0–1.5) | 1 (1–1.75) | 18 (6.5–32.5) | 64.4 ± 44.6 |
| PAPA | 1 (0–2) | 2 (0–6) | 1.5 (0–2.25) | 0 (0–1) | 25 (7–36.25) | 56.5 ± 36.9 |
| CRMO | 4.5 (1.75–15) | 15 (4.5–20) | 0 (0–4.5) | 3 (2–4.75) | 12 (10–26) | 72.8 ± 20.2 |
| SchS | 1 (0–2) | 0 (0–0) | 2 (1–3) | 1 (0–1) | 50 (40–50) | 52.4 ± 40.0 |
| AOSD | 4 (0.75–10) | 0 (0–2.5) | 1 (1–4) | 10 (6–15) | 31.5 (24.75–40) | 73.3 ± 19.1 |
| SJIA | 5 (2–12) | 12 (2–20) | 5 (0.5–9) | 5 (2–7) | 9 (6.25–12) | 62.3 ± 25.7 |
| PG | 3 (0–10.5) | 0 (0–0.25) | 12 (4–20) | 2 (0–4) | 55 (40–60) | 60.7 ± 25.4 |
| BD | 5 (1–10) | 1 (0.5–2) | 5 (2–10) | 10 (4–15) | 30 (15–35) | 53.6 ± 34.2 |