Table 1.

Demographics and clinical characteristics of children with sickle cell disease at time of first audiogram, 2010–2016.

Parameter	Number of Patients (total n = 181) (%)	Mean ± SD (Range)
Mean age at first audiogram (years)	181	8.9 ± 5.2 (0–19.6)
Mean # of audiograms received	181	1.5 ± 1 (1–9)
SCD Genotype: HbSS	153 (84.5%)
SCD Genotype: HbS Beta Thalassemia	9 (5.0%)
Sex (male)	97 (53.6%)
Newborn hearing screen:	174 (96.1%)
- Passed	167 (96.0%)
- Failed	7 (4.0%)
Indication for audiology test:	181 (100%)
- Hearing concern	48 (26.5%)
- History of cerebrovascular accident	5 (2.8%)
- History of ototoxic medication regimen	105 (58.0%)
- History of recurrent ear infections	9 (5.0%)
- To establish a hearing baseline	14 (7.7%)
Indication for transfusion:
- History of cerebrovascular accident (yes)	54 (29.8%)
- Abnormal transcranial doppler (yes)	46 (25.4%)
- On chronic transfusion therapy (yes)	101 (55.8%)
- SNHL	12 (6.6%)