. 2019 Jan-Feb;23(1):159–164. doi: 10.4103/ijem.IJEM_252_18

Table 1.

Table summarizing the five cases

	Case 1	Case 2	Case 3	Case 4	Case 5
Age/Sex	11/F	7/M	16/M	26/M	30/F
Clinical presentation	hypertension	hypertension	Sudden quadriparesis	Hemicranial headache	Progressive spastic quadriparesis

Tumors

Pheochromocytoma	+	+	+	+	--
Renal Cell Carcinoma	-	-	-	-	+
Hemangioblastoma	-	-	+	+	+
Others	-	-	Pancreatic and renal cysts	Pancreatic neuroendocrine tumor	Pancreatic cyst
Mutation	+	+	+	+	-
Type of VHL	2C	2C	2A	2A	I
Family history	+	+	+	+	+
Surgery performed	Staged b/l adrenalectomy	Bilateral adrenalectomy	Bilateral adrenalectomy	Unilateral adrenalectomy Pancreaticoduodenectomy	Radical nephrectomy
Surgery performed	Staged b/l adrenalectomy	Bilateral adrenalectomy	Excision of hemangioblastoma	Excision of hemangioblastoma	Excision of hemangiobalstoma
Histopathology	Pheochromocytoma without hyperplasia	Pheochromocytoma without hyperplasia	Pheochromocytoma without hyperplasia	Pheochromocytoma without hyperplasia NET with unncertain malignant potential
Outcome	Asymptomatic	Asymptomatic	Post-operative mortality	Asymptomatic	Asymptomatic