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. Author manuscript; available in PMC: 2019 Apr 3.
Published in final edited form as: J Immunol Sci. 2018 Aug 2;Suppl:146–150.

Table 5.

Clinical presentation in the 119 confirmed cases of CRS in 5 countries. 2012 – 2016.

Clinical sign Number of cases % cases
Group A Congenital Heart Disease 86 72%
Cataracts 38 32%
Glaucoma 12 10%
Hearing impairment 6 5%
Pigmentary retinopathy 1 1%
Group B Microcephaly 40 34%
Splenomegaly 30 25%
Jaundice 16 13%
Purpura 14 12%
Mental retardation 10 8%
Meningo-encephalitis 4 3%
Radiolucent bone disease 0 0%