Table 2.

Glucosylsphingosine levels (pmol/mg tissues).

Mouse models	Age	Liver	Lung	Spleen	Brain
WT	<1 day	un	un	ND	un
WT	6 weeks	un	un	un	1.7 ± 0.1
WT	52 weeks	un	un	un	2.7 ± 0.3
9V;C*	<1 day	1.2 ± 0.1	1.9 ± 0.7	ND	0.7 + 0.0
0S;C*	<1 day	un	0.9 ± 0.1	ND	un
4L;C*	6 weeks	1.5 ± 0.4	1.9 ± 0.9	2.4 ± 0.2	12.3 ± 0.2^
9H;C*	52 weeks	un	un	1.6 ± 0.7	5.4 ± 0.3^

un, undetectable.

^{^}significant difference compared to age-matched WT.

ND, not determined.