Table 1.
Demographics of CJD population
| n | Female, n (%) | Age at death (mean years ± SD) | Duration (mean months ± SD) | |
|---|---|---|---|---|
| Total CJD cases | 450 | 234 (52.0) | 68.1 ± 9.0 | 7.4 ± 11.6 |
| Histotypea | ||||
| MM(V)1 | 329 | 159 (48.3) | 68.9 ± 8.6 | 5.5 ± 9.2 |
| VV2 | 61 | 36 (59.0) | 67.5 ± 9.1 | 7.4 ± 8.3 |
| MV2K | 38 | 24 (63.1) | 65.2 ± 8.3 | 16.7 ± 12.8 |
| MM2C | 13 | 10 (77.0) | 66.8 ± 9.5 | 16.0 ± 13.5 |
| MM2T | 4 | 2 (50.0) | 48.5 ± 14.6 | 20.0 ± 12.6 |
| VV1 | 2 | 1 (50.0) | 65.5 ± 0.7 | 9.8 ± 5.3 |
| VPSPr | 2 | 1 (50.0) | 76.5 ± 2.1 | 21.0 ± 21.2 |
| PrPSc typeb | ||||
| 1 | 241 | 110 (45.6) | – | – |
| 1 + 2 | 101 | 57 (56.4) | – | – |
| 2 | 106 | 66 (62.3) | – | – |
| Codon 129 | ||||
| MM | 326 | 164 (50.3) | – | – |
| MV | 60 | 32 (53.3) | – | – |
| VV | 64 | 38 (59.4) | – | – |
aOne atypical case was not included
bTwo VPSPr cases were not included