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. Author manuscript; available in PMC: 2020 Feb 1.
Published in final edited form as: Am J Ophthalmol. 2018 Oct 31;198:223–261. doi: 10.1016/j.ajo.2018.10.022

TABLE 16.

Cumulative Incidence of Progression to Advanced Age-Related Macular Degeneration at 2, 5, 10, and 12 Years Based on the Composite Risk Score, Adjusting for Mortality Risks for a Representative Sample of 24 Right and Left Eyes with Intermediate Stage Disease at Baseline.

1 2 3 4 5 6 7 8 9 10 11 12
Eye OD OD OD OD OD OD OD OD OD OD OD OD
Age 65-74 ≥ 75 ≥ 75 ≥ 75 < 65 ≥ 75 ≥ 75 ≥ 75 65-74 65-74 65-74 65-74
Sex F M M M F F F F M F F F
Education > HS ≤ HS ≤ HS > HS ≤ HS ≤ HS ≤ HS ≤ HS ≤ HS ≤ HS ≤ HS > HS
Body mass index 25-29 ≥ 30 25-29 < 25 ≥ 30 25-29 < 25 25-29 ≥ 30 ≥ 30 ≥ 30 < 25
Smoking Never Never Past Past Never Never Never Never Past Past Never Current

Complement pathway
CFH Y402H: rs1061170 TT CT CC CC TT CT CT CT TT CC CC TT
CFH: rs1410996 TT CT CC CC CT CT CT CC CT CC CC CT
CFH R1210C: rs121913059 CC CC CC CC CT CC CC CC CC CC CC CC
C2 E318D: rs9332739 GG GG GG GG GG GG GG GG GG GG GG GG
CFB R32Q: rs641153 CC CC CC CC CC CC CC CC CT CC CC CC
C3 R102G: rs2230199 CG CG CC CC CC CG GG CC CC CC CC CG
C3 K155Q: rs147859257 TT GT TT TT TT TT TT TT TT TT TT TT
Immune/inflammatory pathway
ARMS2/HTRA1: rs10490924 GT GT GG TT GT GG GT GT GT GT GT GT
PELI3: rs145732233 CC CC CC CC CC CC CT CC CC CC CC CC
Extracellular matrix
COL8A1: rs13095226 TT CT TT CT TT TT TT TT CT TT TT CT
CTRB1: rs8056814 GG GG GG GG GG GG GG GG GG GG GG GG
DNA repair/protein binding
RAD51B: rs8017304 GA GA AA AA AA AA AA GG GA AA GG AA
HSPH1/B3GALTL: rs9542236 CT CT CT CT TT TT CT CT CT CT TT CT

2 year cumulative incidence, % 4.2 27.1 14.1 20.6 21.6 8.1 5.1 11.7 6.6 19.4 10.2 15
5 year cumulative incidence, % 10.6 52.1 30.4 40.8 47.8 19 12.3 26.1 16.3 42.4 24.4 34.6
10 year cumulative incidence, % 21.1 67.6 45.4 54.4 76.7 32.6 22.1 41.1 31.5 65.6 44.4 58.6
12 year cumulative incidence, % 25.5 69.4 48.5 56.2 84.3 36.7 25.4 44.5 37.6 71 51.3 65.7
5 year cumulative incidence no genes, % 19.6 31 31.3 21.7 23.5 29.3 26.2 28.3 32.7 34.3 28.9 32.4
13 14 15 16 17 18 19 20 21 22 23 24

Eye OS OS OS OS OS OS OS OS OS OS OS OS
Age 65-74 < 65 65-74 65-74 65-74 ≥ 75 65-74 65-74 ≥ 75 65-74 65-74 < 65
Sex F F F F F M F M F M F M
Education > HS > HS ≤ HS > HS ≤ HS > HS ≤ HS ≤ HS > HS ≤ HS > HS > HS
Body mass index ≥ 30 ≥ 30 < 25 25-29 25-29 < 25 < 25 25-29 25-29 25-29 25-29 25-29
Smoking Past Past Never Past Past Past Never Never Never PAST Past Current

Complement pathway
CFH Y402H: rs1061170 CC CT TT CC CT CC CC CC CC CT CC CT
CFH: rs1410996 CC CT CT CC CT CC CC CC CC CC CC CC
CFH R1210C: rs121913059 CC CC CC CC CT CC CC CC CC CC CC CC
C2 E318D: rs9332739 GG GG GG GG GG GG GG GG GG GG GG GG
CFB R32Q: rs641153 CC CC CC CC CC CT CC CC CC CC CC CC
C3 R102G: rs2230199 CG CG CG CG CG CC GG CC CG CC CC CC
C3 K155Q: rs147859257 TT GT TT TT TT TT TT TT TT TT TT TT
Immune/inflammatory pathway
ARMS2/HTRA1: rs10490924 GG TT GG TT GG GG GG GT GG GT GG GG
PELI3: rs145732233 CC CC CC CC CC CC CT CC CC CC CC CC
Extracellular matrix
COL8A1: rs13095226 TT TT TT TT TT CT TT TT CT TT TT TT
CTRB1: rs8056814 GG GG GG GG GG AG GG GG AG GG GG GG
DNA repair/protein binding
RAD51B: rs8017304 GA AA GG GG GA GA GG AA AA GA GG GG
HSPH1/B3GALTL: rs9542236 CC TT TT CC CT TT CC CT CT CC TT CT

2 year cumulative incidence, % 13.7 20 3.6 18.7 28.7 4.4 4.5 12.6 11.8 11.5 6.1 7.3
5 year cumulative incidence, % 32 45 9.3 40.9 58.7 10.5 11.3 29.1 26.2 27.2 15.2 18.2
10 year cumulative incidence, % 55.3 73.9 19.5 63.4 83.6 18.8 22.4 49.6 41.1 48 30.5 36.7
12 year cumulative incidence, % 62.6 82 24.3 68.6 88 21.5 27 55.8 44.6 54.9 37.1 44.8
5 year cumulative incidence no genes, % 28.6 23.1 22.3 23.5 30.6 23.6 24.4 22.4 22.9 22.4 24.6 27.6

Results shown for derivation cohort. F = Female; M =Male; HS = high school.