Figure 1.

The figure (adapted from Ley et al (2011)[56]) includes a speculative representation of how idiopathic pulmonary fibrosis (IPF) progression might occur from those with an early stage of pulmonary fibrosis (PF) or subclinical disease (left panel). An updated and expanded representation of current knowledge (right panel) which highlights the under-recognised burden of early PF, the risk for accelerated lung function decline and early death^{40 42} even among those not diagnosed with IPF. IIP, idiopathic interstitial pneumonia; ILA, interstitial lung abnormalities.