Table 2.

Summary of assessments, their reliability and internal consistency

Instrument or subscore (reference range)	Mean±SD	Range	Inter-observer reliability (ICC)	Intra-observer or test-retest reliability (ICC)	Cronbach’s alpha
iscorEB clinician (0–114)	11.3±10.9	0–47.1	0.96		0.89
Skin (0–60)	4.1±5.4	0–26.1	0.88	0.91	0.85
Mucosal (0–20)	3.2±2.0	0–8	0.82	0.70	0.88
Internal organ (0–12)	1.6±1.7	0–7	0.97		0.88
Laboratory abnormalities (0–11)	1.5±2.1	0–7	0.98		0.86
Complications / procedures (0–11)	0.9±1.4	0–5	0.91		0.88
BEBS (0–100)	13.4±14.3	0–59	0.96		0.89
iscorEB patient (0–120)	32.4±16.2	0–70	-	0.97	0.84
QOLEB (0–75), N=15	16.3±8.8	2–33	-		0.91
CDLQI (0–30), N=15	11.4±4.9	2–20	-		0.67

SD-standard deviation

BEBS- Epidermolysis Bullosa Severity score

QOLEB- Quality of Life Epidermolysis Bullosa

CDLQI- Childhood Dermatology Life Quality Index