Table 3.
iscorEB portion or domain | Comparison (N=31 unless specified otherwise) Spearman’s rho (p-value) |
---|---|
iscorEB-c versus BEBS (total score) | |
iscorEB-c total score | 0.94 (<.0001) |
Skin | 0.90 (<.0001) |
Mucosal | 0.86 (<.0001) |
Internal organ | 0.73 (<.0001) |
Laboratory abnormalities | 0.83 (<.0001) |
Complications / procedures | 0.77 (<.0001) |
iscorEB-p versus QOLEB (N=15) | 0.91 (<.0001) |
iscorEB-p versus CDLQI (N=15) | 0.76 (0.0009) |
iscorEB-c total score versus iscorEB-p | 0.67 (<.0001) |
Skin | 0.61 (.0003) |
Mucosal | 0.77 (<.0001) |
Internal organ | 0.33 (.067) |
Laboratory abnormalities | 0.63 (.0002) |
Complications / procedures | 0.67 (<.0001) |
BEBS- Epidermolysis Bullosa Severity score
QOLEB- Quality of Life Epidermolysis Bullosa
CDLQI- Childhood Dermatology Life Quality Index