Table 3.
Biochemical features of all samples analyzed.
| Sample # | Clinical Classification of the Disorder | AAT Assay (mg/dL) | Neutrophil Count | Elastase Specific Activity (mU/mg) | Cathepsin G Specific Activity (mU/mg) | Presence of the 80 kDa Complex |
|---|---|---|---|---|---|---|
| 1 | Stable | 0.57 * | 1 | n.d. ** | n.d. ** | NO |
| 2 | Stable | 1.00 | 1 | 0.08 | n.d. | NO |
| 3 | Stable | 0.32 | 1 | n.d. | n.d. | NO |
| 4 | Stable | 0.79 | 34 | 0.725 | n.d. | YES |
| 5 | Stable | 0.37 | 30 | 1.06 | 0.14 | YES |
| 6 | Stable | 0.40 | 1 | n.d. | n.d. | YES |
| 7 | BOS 0p | 0.26 | 28 | 0.29 | n.d. | YES |
| 8 | BOS II | 2.50 | 94 | 4.44 | 0.57 | YES |
| 9 | BOS II | 0.56 | 56 | 2.16 | 0.254 | YES |
| 10 | BOS II | 0.12 | 40 | 2.98 | n.d. | YES |
| 11 | BOS II | 0.12 | 5 | 2.23 | n.d. | YES |
| 12 | BOS III | 0.13 | 10 | n.d. | n.d. | YES |
| 13 | BOSIII | 0.13 | 15 | 1.56 | n.d. | YES |
* Values reported are the mean of three independent determinations. Standard deviation was within 5%. ** n.d. = not detectable.