. 2019 Mar 8;7(5):e00617. doi: 10.1002/mgg3.617

Table 2.

The demographic data and ophthalmologic characteristics of nine Taiwanese patients with MPS I

No.	MPS type	Gender	Age (years)	Right eye or left eye	Visual acuity	Sphere	Cylinder	Axis of cylinder	Refraction (spherical equivalent)	Amblyopia	Corneal opacity	Lens opacity	Optic disc	IOP (mmHg)	Retinal appearance	VEP
I‐1	IH	F	8.3	R	0.6 (6/10)	+1.5	+0.5	150	+1.75	Y	+	Normal	Mild swelling	‐	Normal	Bilateral delay
I‐1	IH	F	8.3	L	0.5 (6/12)	+2.0	+0.75	450	+2.38	Y	+	Normal	Mild swelling	‐	Normal	Bilateral delay
I‐2	IH/S	F	1.6	R	Follow light	‐	‐	‐	‐	N	++	Normal	Normal	‐	Normal	‐
I‐2	IH/S	F	1.6	L	Follow light	‐	‐	‐	‐	N	++	Normal	Normal	‐	Normal	‐
I‐3	IH/S	F	2.2	R	Follow light	No target	No target	No target	No target	N	+	Normal	Normal	‐	Normal	Normal
I‐3	IH/S	F	2.2	L	Follow light	+2.25	−4.0	170	+0.25	N	+	Normal	Normal	‐	Normal	Normal
I‐4	IH/S	M	18.2	R	ND	‐	‐	‐	‐	N	++	‐	Normal	32.7	Poor view	Bilateral no response
I‐4	IH/S	M	18.2	L	ND	‐	‐	‐	‐	N	++	‐	Normal	28.3	Poor view	Bilateral no response
I‐5	IH/S	M	18.9	R	HM/20 cm	No target	No target	No target	No target	N	+++	Total opacity	Swelling	58	Poor view	R mild delay
I‐5	IH/S	M	18.9	L	ND/10 cm	+7.25	+1.75	70	+8.13	N	+++	Slight opacity	Normal	62	Poor view	R mild delay
I‐6	IS	M	13.2	R	1.0 (6/6)	+2.25	+2.25	85	+3.38	N	+	Nuclear sclerosis	Normal	18.1	RPE change	‐
I‐6	IS	M	13.2	L	0.9 (6/6.7)	+2.00	+2.25	90	+3.13	N	+	Nuclear sclerosis	Normal	14.3	RPE change	‐
I‐7	IS	F	22.1	R	0.4 (6/15)	+5.0	+2.0	90	+6.00	Y	+	Normal	Normal	14	Foldings around macula	‐
I‐7	IS	F	22.1	L	0.6 (6/10)	+5.25	+2.25	95	+6.38	Y	+	Normal	Normal	13.5	Foldings around macula	‐
I‐8	IS	M	32.3	R	0.4 (6/15)	+2.0	+1.5	90	+2.75	N	+	Normal	Normal	15.8	RPE change	Bilateral mild delay
I‐8	IS	M	32.3	L	0.7 (6/8.6)	+2.0	+2.0	90	+3.00	N	+	Normal	Normal	20	RPE change	Bilateral mild delay
I‐9	IS	M	34.9	R	0.8 (6/7.5)	+9.0	+1.5	140	+9.75	N	+	Nuclear sclerosis	Normal	14.3	Normal	‐
I‐9	IS	M	34.9	L	0.3 (6/20)	+9.0	+1.5	90	+9.75	Y	+	Nuclear sclerosis	Normal	15.3	Normal	‐

Notes. MPS, mucopolysaccharidosis; IOP, intraocular pressure; VEP, visual evoked potential; H, Hurler; H/S, Hurler/Scheie; S, Scheie; F, female; M, male; R, right; L, left; ND, digit number; HM, hand motion; ‐, not assessed; Y, yes; N, no; +, mild corneal clouding; ++, moderate corneal clouding; +++, severe corneal clouding; RPE, retinal pigment epithelial.